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Rafael Martinez-Sanz

Universidad de La Laguna, Spain

Title: Pulmonary valve spindle-cell lipoma: the rarest cause of the most frequent symptom, dyspnea, resolved by leaflets bicuspidization

Abstract

Primary cardiac tumours are rare and most of them are benign. Myxomas, fibroelastomas, and lipomas are common in adults. Primary valvular cardiac tumours are even more rare and affect all four valves in a similar proportion. Valvular lipomas are very rare. In the pulmonary valve there is only one described. Lipomas can be spindle-cell variety. But of these there is only one described in a valves and it´s in the aortic valve. Pulmonary valve lipomas (PVL) can obstruct the right ventricular outflow tract, cause pulmonary valve regurgitation, or pulmonary embolism. Symptoms may be dyspnea, angina, arrhythmias, or syncope. We present a 54-year-old woman with a giant spindle-cell lipoma located in the anterior pulmonary leaflet, with severe dyspnea. Total resection of the tumour was performed and restoration of valve function was obtained by means of bicuspidization of the remaining pulmonary leaflets. She had a postoperative complication-free clinical evolution beeng dicharged from hospital after seven days from surgery, with echocardiographic control, showing good biventricular function, absence of tumour or obstruction, and minimal pulmonary valve regurgitation. 

Biography

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